{"id":764,"date":"2021-03-08T09:44:41","date_gmt":"2021-03-08T09:44:41","guid":{"rendered":"https:\/\/kinderambulatorium.com\/?p=764"},"modified":"2025-06-23T14:49:03","modified_gmt":"2025-06-23T12:49:03","slug":"mittelmeerfieber-kinderambulatorium","status":"publish","type":"post","link":"https:\/\/kinderambulatorium.com\/tr\/mittelmeerfieber-kinderambulatorium\/","title":{"rendered":"Ailesel Akdeniz ate\u015fi"},"content":{"rendered":"<div data-elementor-type=\"wp-post\" data-elementor-id=\"764\" class=\"elementor elementor-764\" data-elementor-settings=\"{&quot;ha_cmc_init_switcher&quot;:&quot;no&quot;}\" data-elementor-post-type=\"post\">\n\t\t\t\t\t\t<section class=\"elementor-section elementor-top-section elementor-element elementor-element-36497cc4 elementor-section-boxed elementor-section-height-default elementor-section-height-default\" data-id=\"36497cc4\" data-element_type=\"section\" data-e-type=\"section\" data-settings=\"{&quot;_ha_eqh_enable&quot;:false}\">\n\t\t\t\t\t\t<div class=\"elementor-container elementor-column-gap-default\">\n\t\t\t\t\t<div class=\"elementor-column elementor-col-100 elementor-top-column elementor-element elementor-element-6f4a7a1a\" data-id=\"6f4a7a1a\" data-element_type=\"column\" data-e-type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-be3abea elementor-widget elementor-widget-text-editor\" data-id=\"be3abea\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t<h3>Ailesel Akdeniz ate\u015fi<\/h3><h4 class=\"p1\">\u00a0<\/h4><p class=\"p2\">Ailevi Akdeniz Ate\u015fi (FMF), s\u0131kl\u0131kla \u015fiddetli kar\u0131n a\u011fr\u0131s\u0131 ile ili\u015fkilendirilen periyodik bir ate\u015f sendromudur. G\u00f6\u011f\u00fcs a\u011fr\u0131s\u0131, eklem a\u011fr\u0131s\u0131 veya deri d\u00f6k\u00fcnt\u00fcleri de daha az yayg\u0131nd\u0131r. Etkilenenlerin \u00e7o\u011fu Akdeniz k\u00f6kenli insanlard\u0131r (Sefarad Yahudileri, Kuzey Afrika Araplar\u0131, Ermeniler, Yunanl\u0131lar, \u0130talyanlar ve T\u00fcrkler gibi).<\/p><p class=\"p2\">Ailesel Akdeniz ate\u015finden etkilenen hastalar\u0131n 50&#039;ye kadar %&#039;si, hastal\u0131\u011f\u0131 ta\u015f\u0131yan akrabalar\u0131, \u00e7o\u011funlukla karde\u015fleri, yani spesifik genetik kusur.<\/p><h4 class=\"p1\">Semptomlar<\/h4><p class=\"p2\">Hastalar\u0131n yakla\u015f\u0131k 95%&#039;si aral\u0131kl\u0131 kar\u0131n a\u011fr\u0131s\u0131 ve y\u00fcksek ate\u015f (40 \u00b0 C&#039;ye kadar) ataklar\u0131na sahiptir. Bu \u00e7ok a\u011fr\u0131l\u0131 semptomlar genellikle 24 ila 72 saat, bazen daha uzun s\u00fcrer. Olu\u015f s\u0131kl\u0131\u011f\u0131 de\u011fi\u015fiklik g\u00f6sterir: \u00e7ok \u015fiddetli vakalarda, n\u00f6betler haftada iki defaya kadar veya yaln\u0131zca y\u0131lda bir kez tekrarlayabilir. N\u00fckslerin \u015fiddeti ve s\u0131kl\u0131\u011f\u0131 ya\u015fla veya hamilelik s\u0131ras\u0131nda azalabilir. Bazen alevlenmeler birka\u00e7 y\u0131l boyunca tamamen durur ve sonra ba\u015ftan ba\u015flar.<span class=\"Apple-converted-space\">\u00a0<\/span><\/p><p class=\"p2\">En korkun\u00e7 komplikasyon, birinin geli\u015fmesidir. <a href=\"https:\/\/www.msdmanuals.com\/de\/heim\/hormon-und-stoffwechselerkrankungen\/amyloidose\/amyloidose\" target=\"_blank\" rel=\"noopener\"><span class=\"s1\">Amiloidoz<\/span><\/a> Tedavi edilmedi\u011fi takdirde gen\u00e7 yeti\u015fkinlikte b\u00f6brek yetmezli\u011fine yol a\u00e7abilen b\u00f6breklerin<\/p><h4 class=\"p1\">terapi<\/h4><p class=\"p2\">G\u00fcnl\u00fck oral kol\u015fisin, a\u011fr\u0131l\u0131 relapslar\u0131 durdurabilir veya insanlar\u0131n yakla\u015f\u0131k y\u00fczde 85&#039;inde relaps say\u0131s\u0131n\u0131 \u00f6nemli \u00f6l\u00e7\u00fcde azaltabilir. Bu, amiloidoz nedeniyle b\u00f6brek yetmezli\u011fi riskini b\u00fcy\u00fck \u00f6l\u00e7\u00fcde azalt\u0131r. Hamile kad\u0131nlarda kol\u015fisin, d\u00fc\u015f\u00fck yapmaya yol a\u00e7abilecek n\u00fcksleri \u00f6nler. Tedavi, tedavinin kesilmesinden sonra amiloidoz riski yeniden artt\u0131\u011f\u0131 i\u00e7in t\u00fcm ya\u015fam boyunca uygulanmal\u0131d\u0131r.<\/p><p class=\"p3\">A\u011fr\u0131 ve ate\u015f i\u00e7in ibuprofen veya parasetamol verilebilir.<\/p><p class=\"p3\">Hasta kol\u015fisine yan\u0131t vermezse biyolojik ila\u00e7lar (canakinumab, anakinra) yard\u0131mc\u0131 olabilir. Bu ila\u00e7lar ba\u011f\u0131\u015f\u0131kl\u0131k sisteminin \u00e7al\u0131\u015fma \u015feklini de\u011fi\u015ftirir ve iltihab\u0131 azalt\u0131r.<\/p><p class=\"p2\">Tutarl\u0131 tedavi ve d\u00fczenli t\u0131bbi kontrollerle, normal bir ya\u015fam beklentisine sahip normal bir ya\u015fam m\u00fcmk\u00fcnd\u00fcr.<\/p>\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t<div class=\"elementor-element elementor-element-fe91744 elementor-widget elementor-widget-button\" data-id=\"fe91744\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"button.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t<div class=\"elementor-button-wrapper\">\n\t\t\t\t\t<a class=\"elementor-button elementor-button-link elementor-size-sm\" href=\"https:\/\/kinderambulatorium.com\/tr\/blog-kinderambulatorium\/\">\n\t\t\t\t\t\t<span class=\"elementor-button-content-wrapper\">\n\t\t\t\t\t\t\t\t\t<span class=\"elementor-button-text\">makalelere geri d\u00f6n<\/span>\n\t\t\t\t\t<\/span>\n\t\t\t\t\t<\/a>\n\t\t\t\t<\/div>\n\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/section>\n\t\t\t\t<\/div>","protected":false},"excerpt":{"rendered":"<p>Das famili\u00e4re Mittelmeerfieber Das famili\u00e4re Mittelmeerfieber (FMF) ist ein periodisch auftretendes Fiebersyndrom, das oft mit starken Bauchschmerzen einhergeht. Seltener treten auch Brustschmerzen, Gelenkschmerzen oder Hautausschl\u00e4ge auf. Betroffen sind vor allem Menschen mit Abstammung aus dem Mittelmeerraum (wie sephardische Juden, nordafrikanische Araber, Armenier, Griechen, Italiener und T\u00fcrken). Bis zu 50\u00a0% der vom famili\u00e4ren Mittelmeerfieber betroffenen Patienten [&hellip;]<\/p>\n","protected":false},"author":1,"featured_media":762,"comment_status":"closed","ping_status":"closed","sticky":false,"template":"","format":"standard","meta":{"site-sidebar-layout":"default","site-content-layout":"default","ast-site-content-layout":"default","site-content-style":"default","site-sidebar-style":"default","ast-global-header-display":"","ast-banner-title-visibility":"","ast-main-header-display":"","ast-hfb-above-header-display":"","ast-hfb-below-header-display":"","ast-hfb-mobile-header-display":"","site-post-title":"","ast-breadcrumbs-content":"","ast-featured-img":"","footer-sml-layout":"","ast-disable-related-posts":"","theme-transparent-header-meta":"default","adv-header-id-meta":"","stick-header-meta":"default","header-above-stick-meta":"","header-main-stick-meta":"","header-below-stick-meta":"","astra-migrate-meta-layouts":"set","ast-page-background-enabled":"default","ast-page-background-meta":{"desktop":{"background-color":"","background-image":"","background-repeat":"repeat","background-position":"center center","background-size":"auto","background-attachment":"scroll","background-type":"","background-media":"","overlay-type":"","overlay-color":"","overlay-opacity":"","overlay-gradient":""},"tablet":{"background-color":"","background-image":"","background-repeat":"repeat","background-position":"center center","background-size":"auto","background-attachment":"scroll","background-type":"","background-media":"","overlay-type":"","overlay-color":"","overlay-opacity":"","overlay-gradient":""},"mobile":{"background-color":"","background-image":"","background-repeat":"repeat","background-position":"center center","background-size":"auto","background-attachment":"scroll","background-type":"","background-media":"","overlay-type":"","overlay-color":"","overlay-opacity":"","overlay-gradient":""}},"ast-content-background-meta":{"desktop":{"background-color":"var(--ast-global-color-5)","background-image":"","background-repeat":"repeat","background-position":"center center","background-size":"auto","background-attachment":"scroll","background-type":"","background-media":"","overlay-type":"","overlay-color":"","overlay-opacity":"","overlay-gradient":""},"tablet":{"background-color":"var(--ast-global-color-5)","background-image":"","background-repeat":"repeat","background-position":"center center","background-size":"auto","background-attachment":"scroll","background-type":"","background-media":"","overlay-type":"","overlay-color":"","overlay-opacity":"","overlay-gradient":""},"mobile":{"background-color":"var(--ast-global-color-5)","background-image":"","background-repeat":"repeat","background-position":"center center","background-size":"auto","background-attachment":"scroll","background-type":"","background-media":"","overlay-type":"","overlay-color":"","overlay-opacity":"","overlay-gradient":""}},"footnotes":""},"categories":[16],"tags":[13,11,14],"class_list":["post-764","post","type-post","status-publish","format-standard","has-post-thumbnail","hentry","category-ambulanz","tag-behandlungen","tag-fieber","tag-urlaub"],"_links":{"self":[{"href":"https:\/\/kinderambulatorium.com\/tr\/wp-json\/wp\/v2\/posts\/764","targetHints":{"allow":["GET"]}}],"collection":[{"href":"https:\/\/kinderambulatorium.com\/tr\/wp-json\/wp\/v2\/posts"}],"about":[{"href":"https:\/\/kinderambulatorium.com\/tr\/wp-json\/wp\/v2\/types\/post"}],"author":[{"embeddable":true,"href":"https:\/\/kinderambulatorium.com\/tr\/wp-json\/wp\/v2\/users\/1"}],"replies":[{"embeddable":true,"href":"https:\/\/kinderambulatorium.com\/tr\/wp-json\/wp\/v2\/comments?post=764"}],"version-history":[{"count":11,"href":"https:\/\/kinderambulatorium.com\/tr\/wp-json\/wp\/v2\/posts\/764\/revisions"}],"predecessor-version":[{"id":5306,"href":"https:\/\/kinderambulatorium.com\/tr\/wp-json\/wp\/v2\/posts\/764\/revisions\/5306"}],"wp:featuredmedia":[{"embeddable":true,"href":"https:\/\/kinderambulatorium.com\/tr\/wp-json\/wp\/v2\/media\/762"}],"wp:attachment":[{"href":"https:\/\/kinderambulatorium.com\/tr\/wp-json\/wp\/v2\/media?parent=764"}],"wp:term":[{"taxonomy":"category","embeddable":true,"href":"https:\/\/kinderambulatorium.com\/tr\/wp-json\/wp\/v2\/categories?post=764"},{"taxonomy":"post_tag","embeddable":true,"href":"https:\/\/kinderambulatorium.com\/tr\/wp-json\/wp\/v2\/tags?post=764"}],"curies":[{"name":"wp","href":"https:\/\/api.w.org\/{rel}","templated":true}]}}